Autopsy and Case Reports
Autopsy and Case Reports
Clinical Case Report

Rare association between giant-cell aortitis and giant-cell aortic valvulitis

Georgina del Cisne Jadán Luzuriaga; Ricardo Ribeiro Dias; José Augusto Duncan Santiago; Vagner Madrini Junior; Walther Yoshiharu Ishikawa; Fabio Fernandes; Vera Demarchi Aiello

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Giant cell arteritis (GCA) is a type of chronic vasculitis that affects medium and large-caliber arteries, frequently related to aortic involvement and, consequently, to aneurysm formation. However, associated valvulitis with giant cells is uncommon. We describe the case of a 50-year-old female patient with aortic aneurysm and valvular insufficiency, whose anatomopathological examination revealed giant-cell aortic valvulitis associated with giant cell aortitis.


Aorta, Thoracic, Aortic Diseases, Aortic Aneurysm, Aortic Valve, Aortic Valve Insufficiency


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