Autopsy and Case Reports
Autopsy and Case Reports
Clinical Case Report and Review

Pindborg tumor associated with a supernumerary tooth: a case report

Hannah Gil de Farias Morais; Weslay Rodrigues da Silva; Ana Cláudia de Macêdo Andrade; Nelmara Sousa e Silva; Mariana Carvalho Xerez; José Wittor de Macêdo Santos; Adriano Rocha Germano; Antônio de Lisboa Lopes Costa

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The calcifying epithelial odontogenic tumor is a rare benign neoplasm that accounts for approximately 1% of all odontogenic tumors. Most of the cases occur in the posterior mandible, and a few involve the maxilla. Despite their relatively indolent biological behavior, tumors in the maxilla tend to grow fast. We report the case of a 33-year-old female patient exhibiting swelling in the right maxilla. An isodense area associated with an impacted supernumerary tooth was found on imaging examination. The histopathologic diagnosis was a calcifying epithelial odontogenic tumor. The treatment of choice was surgical removal of the lesion and associated dental elements. The patient has been followed up for 11 months and shows no signs of recurrence. Besides describing this case, we reviewed the literature on the association of calcifying epithelial odontogenic tumors with supernumerary teeth and found two case reports addressing this subject.


Odontogenic Tumors, Dental Tissue Neoplasms, Calcifying Epithelial Odontogenic Tumor, Pindborg tumor


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