Autopsy and Case Reports
https://autopsyandcasereports.org/article/doi/10.4322/acr.2021.308
Autopsy and Case Reports
Clinical Case Report and Review

Renal angiomyolipoma with epithelial cyst

Bharti Varshney; Vikarn Vishwajeet; Vijay Madduri; Gautam Ram Chaudhary; Poonam Abhay Elhence

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Abstract

Angiomyolipoma with epithelial cysts (AMLEC) is a recently described entity and is an uncommon subtype of kidney angiomyolipomas. AMLEC is a benign entity but usually masquerades a renal cell carcinoma on imaging examination. AMLEC has a distinct histological and immunohistochemical staining pattern, which helps in the pathological diagnosis. We present a rare case of AMLEC in a 26-year-old female, which was provisionally diagnosed as renal cell carcinoma on radiology. We also summarize the differential diagnosis of this rare variant, its characteristic features, and a review of the literature.

Keywords

Angiomyolipoma, Neoplasms, Kidney, Nephrectomy, Diagnosis, Differential

References

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Submitted date:
02/01/2021

Accepted date:
06/17/2021

Publication date:
08/20/2021

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