Autopsy and Case Reports
https://autopsyandcasereports.org/article/doi/10.4322/acr.2021.259
Autopsy and Case Reports
Clinical Case Report and Review

Giant virilising adrenal cortical carcinoma

Shruti Dogra; Arvind Ahuja; Minakshi Bhardwaj; Rohan Sardana; Hemant Goel

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Abstract

Androgen secreting adrenocortical carcinoma (ACC) is a very rare disease with a poor prognosis. Approximately 80% of tumors are functional, most commonly secreting glucocorticoids. We herewith report a case of a huge functional ACC of the right adrenal gland in a 33-year-old female who presented with complaints of hirsutism, amenorrhea and an abdominal lump. On abdominal examination a large lump was palpable in the right hypochondrium reaching up to the umbilicus. Contrast-enhance computed tomography (CECT) revealed a mass in the right suprarenal region. The tumor measured 29 cm × 20 cm × 12 cm and weighed 7.8 kg, the largest reported case of ACC in the world to the best of our knowledge.

Keywords

Adrenocortical carcinoma, Adrenal Gland, Functional, Giant, Largest

References

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Submitted date:
01/01/2021

Accepted date:
02/01/2021

Publication date:
05/06/2021

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