Autopsy and Case Reports
https://autopsyandcasereports.org/article/doi/10.4322/acr.2021.246
Autopsy and Case Reports
Autopsy Case Report

Extranodal NK/T-cell lymphoma, nasal type with extensive cardiopulmonary involvement

Mario L. Marques-Piubelli; Gabriel Teixeira Montezuma Sales; Letícia Campos Clemente; Lidiane Inês Rosa; Mariana Lorenzi Savioli; Ricardo Pires Alvim; Raquel Megale Moreira; Fernando Pereira Frassetto; Ellen Caroline Toledo do Nascimento; Sheila Aparecida Coelho Siqueira

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Abstract

Extranodal NK/T-cell lymphoma, nasal type (ENKTL-NT) is a rare type of Non-Hodgkin’s lymphoma, which usually presents with extranodal involvement and affects the nasal/upper aerodigestive tract in the classical presentation. Herein, we report the case of a 31-year-old, previously healthy, male patient diagnosed with ENKTL-NT with the involvement of the lung parenchyma and heart. Unfortunately, due to the rapid disease progression, the diagnosis was performed only at the autopsy. The authors highlight the rare clinical presentation of this type of lymphoma, as well as the challenging anatomopathological diagnosis in necrotic samples.

Keywords

Lymphoma, Extranodal NK-T-Cell, Epstein-Barr Virus Infections, Lymphoma, Lymphoma, Non-Hodgkin

References

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Submitted date:
10/31/2020

Accepted date:
11/28/2020

Publication date:
03/23/2021

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