Autopsy and Case Reports
https://autopsyandcasereports.org/article/doi/10.4322/acr.2020.155
Autopsy and Case Reports
Article / Autopsy Case Report

Thoracoabdominal compartment syndrome complicating right-sided diaphragmatic eventration with co-existent unilateral renal agenesis

Sebastian Anebuokhae Omenai; Esther Opeyemi Adebowale; Ifeanyichukwu Dupe Nwanji

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Abstract

Diaphragmatic eventration (DE) associated with intestinal malrotation and renal agenesis is a rare entity. The authors report a case of a 69-year-old man who had symptoms of heart failure. He had a previous imaging diagnosis of right diaphragmatic eventration and dilated cardiomyopathy. He died on the second day after the hospital admission and had a post mortem examination that confirmed complete right diaphragmatic eventration, intestinal malrotation, left renal agenesis, dilated cardiomyopathy, and anteriorly rotated right kidney and had findings suggestive of a thoracoabdominal compartment syndrome. Thoracoabdominal compartment syndrome is described as transmission of abdominal pressure through a defective diaphragm causing compression of the hemithorax viscera and mediastinal shift with a hemodynamic alteration. The association of these anomalies is rare, and the possibility of this finding in a patient with eventration should always be considered.

Keywords

Diaphragmatic Eventration, Compartment Syndrome, Hereditary renal agenesis

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Publication date:
04/02/2020

5e85f1aa0e88253a22a14d48 autopsy Articles
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