Autopsy and Case Reports
http://autopsyandcasereports.org/article/doi/10.4322/acr.2018.022
Autopsy and Case Reports
Article / Autopsy Case Report

Congenital pulmonary airway malformation

Wlamir Pestana Ursini; Cesar Cilento Ponce

Abstract

Congenital pulmonary airway malformation (CPAM) is a developmental malformation of the lower respiratory tract. We report the case of a male newborn diagnosed with cystic lung disease during prenatal ultrasound. A cesarean section was performed at the 32nd gestational week because of premature rupture of the membranes, and soon after the delivery the newborn developed respiratory failure and died. The aim of this study is to report an autopsy case because of its rarity, and to briefly discuss the CPAM subtypes and differential diagnosis of cystic lung diseases of childhood.

Keywords

Cystic Adenomatoid Malformation of Lung, Congenital, Respiratory Distress Syndrome, Newborn, Autopsy

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